ED Clinical Pathway for Evaluation/Treatment of Children with Hemophilia and CHI

Factor Information Sheet

Review patient's dose reminder card, if it is available.

Patients with inhibitors

Factor VIII Deficiency (check brand chosen by family)

Recombinant Factor VIII Products

Dose: Wt in kg x % desired x 0.5 = # of units to be given
Individual factor recovery may vary. Check the patient's dose card.

______kg x ______% x 0.5 = _____units to be given

Alphanate (labeled in Factor VIII and ristocetin units). Use Factor VIII units for hemophilia A.
Dose: Wt in kg X % desired X 0.5 = # of Factor VIII units to be given

______kg x______% x 0.5 = _____Factor VIII units to be given

Factor IX Deficiency Benefix (recombinant Factor IX)

Desired % correction x wt. in kg x 1.4 = # of units to be given

_____% x _____kg x 1.4 = _____units to be given

Von Willebrand Disease

Humate-P

Use ristocetin units for Von Willebrand disease. This product is labeled in ristocetin units and in Factor VIII units. Give no more than 2x target dose as maximum dose.

Desired % correction x wt. in kg divided by 2 = units to be given

_____% x _____kg x 0.5 = _____ristocetin units to be given