Alagille Syndrome Clinical Care Program

The Kidneys and Alagille Syndrome

Approximately 40 to 50 percent of children with AGS have renal (kidney) disease. A variety of structural, function and acquired renal disorders have been identified in children with AGS including:

These conditions require a combination of blood tests, ultrasound and urine tests for diagnosis and evaluation.

These disorders are not usually associated with renal failure. Renal tubular acidosis is an important potential contributor to poor growth in Alagille syndrome. If your child is suspected of having kidney disease, he or she may be referred to a pediatric nephrologist for evaluation.

Visit our Nephrology Web site for more information about the treatment of kidney disorders

Reviewed by: Binita M. Kamath, MD
Date: January 2009

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