Forty years ago, single ventricle heart defects were fatal. Today, the majority of children with single ventricle defects survive. These children undergo a series of two or three operations during the first three years of life. This series of operations, known as staged reconstruction, reconfigure the heart and circulatory system into an altered system, called the Fontan circulation.
Over the past 10 years, early outcomes for patients with hypoplastic left heart syndrome (HLHS) and other single ventricle heart defects have improved dramatically. However, the period between the first operation performed in newborns and the second surgery, called the hemi-Fontan or Glenn operation, remains a very vulnerable time for infants with single ventricle heart defects. Certain events or illnesses may place additional stress on the heart and lungs and increase the risk of complications for these patients.
As a world leader in pediatric cardiac care, the Cardiac Center at The Children’s Hospital of Philadelphia has recognized the importance of a dedicated initiative to focus on the care and monitoring of infants with single ventricle heart defects between the first and second reconstructive operations.
The Infant Single Ventricle Monitoring Program provides care for high-risk infants with single ventricle disease who have had a newborn operation (Norwood, shunt, or Hybrid procedure). Patients are followed in the Program beginning after the newborn operation until they undergo the Glenn operation, whether being cared for in the Hospital or at home.
The mission of the Infant Single Ventricle Monitoring Program is to improve the ultimate outcome for patients with single ventricle heart defects. Our goal is to prevent life-threatening events and improve growth between the first and second heart operations at CHOP. The Program includes:
CHOP's ISVMP team also participates in the National Pediatric Cardiology Quality Improvement Collaborative (NPC-QIC), a project dedicated to improving survival and quality of life of infants with single ventricle heart defects during the interstage period.
This program includes a team of providers who will work closely with parents and community physicians to identify potential risks before they pose a danger. The team includes:
For more information on the Infant Single Ventricle Monitoring Program at CHOP, please call 215-435-6342 or email ISVMP@email.chop.edu.
For a second opinion, cardiac referral, or for more information.
To schedule an outpatient appointment.