Michael J. Palmieri Metabolic Disease Laboratory

Amino Acid Quantitation (Urine)

  • LIS Mnemonic: AAQU

    Collect

    Random Urine Container

    Volume Required

    5.0 mL

    Minimum Required

    2.0 mL

    Transport

    Room temperature

    Stability

    8 hours

    Processing

    Refrigerate if delivery to lab is > 8 hours. Freeze if delivery is >24 hours. If sending specimen from outside CHOP, send on dry ice by overnight courier (Mon-Thurs only).

Days Performed

Monday - Friday

Reported

3-5 days

Reflex Testing

N/A

CPT

82139

Remarks

Special circumstances (cystine determination)may require a 24-hour collection.Amino Acids detected:p-serine,taurine,p-ethanolamine,urea,aspartic acid, oh-proline, threonine, serine, asparagine, glutamate, glutamine, sarcosine, a-amino-adipic, proline, glycine, alanine, citrulline, a-amino butyric, valine, cystine, methionine, cystathionine, isoleucine, leucine, tyrosine, phenylalanine, b-alanine, b-amino isobutyric, homocystine, GABA, ethanolamine, ammonia, oh-lysine, ornitine, lysine,1-me-histidine, histidine, 3-me-histidine, anserine, carnosine, arginine

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