Cardiac Center Publications - 2018

Adang, L., Frank, D., Gilani, A., Takanohashi, A., Ulrick, N., Collins, A., Cross Z, Galambos C, Helman G, Jaanaan U, Keller S, Simon D, Sherbini O, Hanna BD, Vanderver, AL. Aicardi goutières syndrome is associated with pulmonary hypertension. Molecular Genetics and Metabolism. 2018 Dec;125(4): 351–358. https://doi.org/10.1016/j.ymgme.2018.09.004.

Boris JR, Bernadzikowski T. Therapy for fatigue and cognitive dysfunction in postural orthostatic tachycardia syndrome. Cardiol Young. 2018 Dec;28(12):1415-1420. doi:10.1017/S1047951118001415. Epub 2018 Sep 10. PubMed PMID: 30198448.

Boris JR, Bernadzikowski T. Utilisation of medications to reduce symptoms in children with postural orthostatic tachycardia syndrome. Cardiol Young. 2018 Dec;28(12):1386-1392. doi:10.1017/S1047951118001373. Epub 2018 Aug 6. PubMed PMID: 30079848.

Boris JR. Postural orthostatic tachycardia syndrome in children and adolescents. Auton Neurosci. 2018 Dec;215:97-101. doi: 10.1016/j.autneu.2018.05.004. Epub 2018 May 12. Review. PubMed PMID: 29778304.

Herrera A, Vajravelu ME, Givler S, Mitteer L, Avitabile CM, Lord K, De León DD. Prevalence of Adverse Events in Children With Congenital Hyperinsulinism Treated With Diazoxide. J Clin Endocrinol Metab. 2018 Dec 1;103(12):4365-4372. doi: 10.1210/jc.2018-01613. PubMed PMID: 30247666; PubMed Central PMCID: PMC6207144.

Kirschen MP, Blinder J, Dewitt A, Snyder M, Ichord R, Berg RA, Nadkarni V, Topjian A. Bedside clinical neurologic assessment utilisation in paediatric cardiac intensive care units. Cardiol Young. 2018 Dec;28(12):1457-1462. doi: 10.1017/S1047951118001634. Epub 2018 Oct 16. PubMed PMID: 30322413.

Lawrence KM, Hennessy-Strahs S, McGovern PE, Mejaddam AY, Rossidis AC, Baumgarten HD, Bansal E, Villeda M, Han J, Gou Z, Zhao S, Rychik J, Peranteau WH, Davey MG, Flake AW, Gaynor JW, Bartoli CR. Fetal hypoxemia causes abnormal myocardial development in a preterm ex utero fetal ovine model. JCI Insight. 2018 Dec 20;3(24). pii: 124338. doi: 10.1172/jci.insight.124338. [Epub ahead of print] PubMed PMID: 30568044.

Lynch JM, Gaynor JW, Licht DJ. Brain Injury During Transition in the Newborn With Congenital Heart Disease: Hazards of the Preoperative Period. Semin Pediatr Neurol. 2018 Dec;28:60-65. doi: 10.1016/j.spen.2018.05.007. Epub 2018 Jun 20. PubMed PMID: 30522729.

Mavroudis CD, Mensah-Brown KG, Ko TS, Boorady TW, Massey SL, Abend NS, Nicolson SC, Morgan RW, Mascio CE, Gaynor JW, Kilbaugh TJ, Licht DJ. Electroencephalographic Response to Deep Hypothermic Circulatory Arrest in Neonatal Swine and Humans. Ann Thorac Surg. 2018 Dec;106(6):1841-1846. doi: 10.1016/j.athoracsur.2018.06.036. Epub 2018 Jul 30. PubMed PMID: 30071237; PubMed Central PMCID: PMC6330195.

Smith AH, Anand V, Banerjee M, Bates KE, Brunetti MA, Cooper DS, Lehrich J, Mistry KP, Pasquali SK, Shin AY, Tabbutt S, Gaies M. Variation in Case-Mix Adjusted Unplanned Pediatric Cardiac ICU Readmission Rates. Crit Care Med. 2018 Dec;46(12):e1175-e1182. doi: 10.1097/CCM.0000000000003440. PubMed PMID: 30252712; PubMed Central PMCID: PMC6239958. 

Biko DM, Johnstone JA, Dori Y, Victoria T, Oliver ER, Itkin M. Recognition of Neonatal Lymphatic Flow Disorder: Fetal MR Findings and Postnatal MR Lymphangiogram Correlation. Acad Radiol. 2018 Nov;25(11):1446-1450. doi: 10.1016/j.acra.2018.02.020. Epub 2018 Mar 23. PubMed PMID: 29580790.

Chang JC, Xiao R, Mercer-Rosa L, Knight AM, Weiss PF. Child-onset systemic lupus erythematosus is associated with a higher incidence of myopericardial manifestations compared to adult-onset disease. Lupus. 2018 Nov;27(13):2146-2154. doi: 10.1177/0961203318804889. Epub 2018 Oct 14. PubMed PMID: 30318995; PubMed Central PMCID: PMC6207474.

Difusco LA, Helman SM. Quality Over Quantity: Standardization of Pediatric HeartWare Ventricular Assist Device Dressing Changes. ASAIO J. 2018 Nov/Dec;64(6):e181-e186. doi: 10.1097/MAT.0000000000000876. PubMed PMID: 30234506.

DiFusco LA, Patton AM, White RM, Bober CM, Miller KD. Home Is Where the HeartWare Is: Preparing Pediatric Patients and Caregivers for Discharge to Home and Integration Into the Community. ASAIO J. 2018 Nov/Dec;64(6):e166-e171. doi: 10.1097/MAT.0000000000000846. PubMed PMID: 30199384.

Geanacopoulos AT, Savla JJ, Pogoriler J, Piccione J, Phinizy P, DeWitt AG, Blinder JJ, Pinto E, Itkin M, Dori Y, Goldfarb SB. Bronchoscopic and histologic findings during lymphatic intervention for plastic bronchitis. Pediatr Pulmonol. 2018 Nov;53(11):1574-1581. doi: 10.1002/ppul.24161. Epub 2018 Sep 12. PubMedPMID: 30207430.

Himebauch AS, Yehya N, Wang Y, Conlon T, Kilbaugh TJ, McGowan FX, Mercer-Rosa L. Early Right Ventricular Systolic Dysfunction and Pulmonary Hypertension Are Associated With Worse Outcomes in Pediatric Acute Respiratory Distress Syndrome. Crit Care Med. 2018 Nov;46(11):e1055-e1062. doi: 10.1097/CCM.0000000000003358. PubMed PMID: 30095502; PubMed Central PMCID: PMC6185756.

Jolley MA, Hammer PE, Ghelani SJ, Adar A, Sleeper LA, Lacro RV, Marx GR, Nathan M, Harrild DM. Three-Dimensional Mitral Valve Morphology in Children and Young Adults With Marfan Syndrome. J Am Soc Echocardiogr. 2018 Nov;31(11):1168-1177.e1. doi: 10.1016/j.echo.2018.06.009. Epub 2018 Aug 8. PubMed PMID: 30098871; PubMed Central PMCID: PMC6218932.

Jolley MA, Lasso A, Nam HH, Dinh PV, Scanlan AB, Nguyen AV, Ilina A, Morray B, Glatz AC, McGowan FX, Whitehead K, Dori Y, Gorman JH 3rd, Gorman RC, Fichtinger G, Gillespie MJ. Toward predictive modeling of catheter-based pulmonary valve replacement into native right ventricular outflow tracts. Catheterization and cardiovascular interventions : official journal of the Society for Cardiac Angiography & Interventions. 2018; PubMed [journal] PMID: 30444053.

Lopez L, Houyel L, Colan SD, Anderson RH, Béland MJ, Aiello VD, Bailliard F, Cohen MS, Jacobs JP, Kurosawa H, Sanders SP, Walters HL 3rd, Weinberg PM, Boris JR, Cook AC, Crucean A, Everett AD, Gaynor JW, Giroud J, Guleserian KJ, Hughes ML, Juraszek AL, Krogmann ON, Maruszewski BJ, St Louis JD, Seslar SP, Spicer DE, Srivastava S, Stellin G, Tchervenkov CI, Wang L, Franklin RCG. Classification of Ventricular Septal Defects for the Eleventh Iteration of the International Classification of Diseases-Striving for Consensus: A Report From the International Society for Nomenclature of Paediatric and Congenital Heart Disease. Ann Thorac Surg. 2018 Nov;106(5):1578-1589. doi: 10.1016/j.athoracsur.2018.06.020. Epub 2018 Jul 19. PubMed PMID: 30031844.

Menachem JN, Lindenfeld J, Schlendorf K, Shah AS, Bichell DP, Book W, Brinkley DM, Danter M, Frischhertz B, Keebler M, Kogon B, Mettler B, Rossano J, Sacks SB, Young T, Wigger M, Zalawadiya S. Center volume and post-transplant survival among adults with congenital heart disease. J Heart Lung Transplant. 2018 Nov;37(11):1351-1360. doi: 10.1016/j.healun.2018.07.007. Epub 2018 Aug 31. PubMed PMID: 30174166.

O'Byrne ML, Glatz AC, Song L, Griffis HM, Millenson ME, Gillespie MJ, Dori Y, DeWitt AG, Mascio CE, Rome JJ. Association Between Variation in Preoperative Care Before Arterial Switch Operation and Outcomes in Patients With Transposition of the Great Arteries. Circulation. 2018 Nov 6;138(19):2119-2129. doi: 10.1161/CIRCULATIONAHA.118.036145. PubMed PMID: 30474422; PubMed Central PMCID: PMC6261315.

Savla JJ, Fisher BT, Faerber JA, Huang YV, Mercer-Rosa L. Complete Versus Staged Repair for Neonates With Tetralogy of Fallot: Establishment and Validation of a Cohort of 2235 Patients Using Detailed Surgery Sequence Review of Health Care Administrative Data. Med Care. 2018 Nov;56(11):e76-e82. doi:10.1097/MLR.0000000000000846. PubMed PMID: 29240000.

Tate J, Stinstra J, Pilcher T, Poursaid A, Jolley MA, Saarel E, Triedman J, MacLeod RS. Measuring defibrillator surface potentials: The validation of a predictive defibrillation computer model. Comput Biol Med. 2018 Nov 1;102:402-410. doi: 10.1016/j.compbiomed.2018.08.025. Epub 2018 Aug 29. PubMed PMID: 30195579; PubMed Central PMCID: PMC6221557.

Anselmo W, Branchetti E, Grau JB, Li G, Ayoub S, Lai EK, Rioux N, Tovmasyan A, Fortier JH, Sacks MS, Batinic-Haberle I, Hazen SL, Levy RJ, Ferrari G. Porphyrin-Based SOD Mimic MnTnBu OE -2-PyP(5+) Inhibits Mechanisms of Aortic Valve Remodeling in Human and Murine Models of Aortic Valve Sclerosis. J Am Heart Assoc. 2018 Oct 16;7(20):e007861. doi: 10.1161/JAHA.117.007861. PubMed PMID: 30371255.

Campbell IM, Sheppard SE, Crowley TB, McGinn DE, Bailey A, McGinn MJ, Unolt M, Homans JF, Chen EY, Salmons HI, Gaynor JW, Goldmuntz E, Jackson OA, Katz LE, Mascarenhas MR, Deeney VFX, Castelein RM, Zur KB, Elden L, Kallish S, Kolon TF, Hopkins SE, Chadehumbe MA, Lambert MP, Forbes BJ, Moldenhauer JS, Schindewolf EM, Solot CB, Moss EM, Gur RE, Sullivan KE, Emanuel BS, Zackai EH, McDonaldMcGinn DM. What is new with 22q? An update from the 22q and You Center at the Children's Hospital of Philadelphia. Am J Med Genet A. 2018 Oct;176(10):2058-2069. doi:10.1002/ajmg.a.40637. PubMed PMID: 30380191.

Chambers DC, Cherikh WS, Goldfarb SB, Hayes D Jr, Kucheryavaya AY, Toll AE, K Khush K, Levvey BJ, Meiser B, Rossano JW, Stehlik J; International Society for Heart and Lung Transplantation. The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Thirty-fifth adult lung and heart-lung transplant report-2018; Focus theme: Multiorgan Transplantation. J Heart Lung Transplant. 2018 Oct;37(10):1169-1183. doi: 10.1016/j.healun.2018.07.020. Epub 2018 Aug 11. PubMed PMID: 30293613.

Cohen MS, Dagincourt N, Zak V, Baffa JM, Bartz P, Dragulescu A, Dudlani G, Henderson H, Krawczeski CD, Lai WW, Levine JC, Lewis AB, McCandless RT, Ohye RG, Owens ST, Schwartz SM, Slesnick TC, Taylor CL, Frommelt PC; Pediatric Heart Network Investigators. The Impact of the Left Ventricle on Right Ventricular Function and Clinical Outcomes in Infants with Single-Right Ventricle Anomalies up to 14 Months of Age. J Am Soc Echocardiogr. 2018 Oct;31(10):1151-1157. doi: 10.1016/j.echo.2018.05.003. Epub 2018 Jul 3. PubMed PMID: 29980396.

Cuneo BF, Sonesson SE, Levasseur S, Moon-Grady AJ, Krishnan A, Donofrio MT, Raboisson MJ, Hornberger LK, Van Eerden P, Sinkovskaya E, Abuhamad A, Arya B, Szwast A, Gardiner H, Jacobs K, Freire G, Howley L, Lam A, Kaizer AM, Benson DW, Jaeggi E. Home Monitoring for Fetal Heart Rhythm During Anti-Ro Pregnancies. J Am Coll Cardiol. 2018 Oct 16;72(16):1940-1951. doi: 10.1016/j.jacc.2018.07.076. Erratum in: JAm Coll Cardiol. 2018 Nov 15. PubMed PMID: 30309472.

DiLorenzo M, Hwang WT, Goldmuntz E, Ky B, Mercer-Rosa L. Diastolic dysfunction in tetralogy of Fallot: Comparison of echocardiography with catheterization. Echocardiography. 2018 Oct;35(10):1641-1648. doi: 10.1111/echo.14113. Epub 2018 Aug 13. PubMed PMID: 30105757; PubMed Central PMCID: PMC6205242.

Eckhauser A, Pasquali SK, Ravishankar C, Lambert LM, Newburger JW, Atz AM, Ghanayem N, Schwartz SM, Zhang C, Jacobs JP, Minich LL. Variation in care for infants undergoing the Stage II palliation for hypoplastic left heart syndrome. Cardiol Young. 2018 Oct;28(10):1109-1115. doi: 10.1017/S1047951118000999. Epub 2018 Jul 24. PubMed PMID: 30039776; PubMed Central PMCID: PMC6156925.

Edelson JB, Rossano JW, Griffis H, Dai D, Faerber J, Ravishankar C, Mascio CE, Mercer-Rosa LM, Glatz AC, Lin KY. Emergency Department Visits by Children With Congenital Heart Disease. J Am Coll Cardiol. 2018 Oct 9;72(15):1817-1825. doi: 10.1016/j.jacc.2018.07.055. PubMed PMID: 30286926.

Goldfarb SB, Hayes D Jr,, Levvey BJ, Cherikh WS, Chambers DC, Khush KK, Kucheryavaya AY, Meiser B, Rossano JW, Stehlik J; International Society for Heart and Lung Transplantation. The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Twenty-first Pediatric Lung and Heart‒Lung Transplantation Report-2018; Focus Theme: Multiorgan Transplantation. J Heart Lung Transplant. 2018 Oct;37(10):1196-1206. doi: 10.1016/j.healun.2018.07.021. Epub 2018 Aug 24. PubMed PMID: 30293615.

Hoskoppal A, Menon S, Trachtenberg F, Burns KM, De Backer J, Gelb BD, Gleason M, James J, Lai WW, Liou A, Mahony L, Olson AK, Pyeritz RE, Sharkey AM, Stylianou M, Wechsler SB, Young L, Levine JC, Tierney ESS, Lacro RV, Bradley TJ; Pediatric Heart Network Investigators. Predictors of Rapid Aortic Root Dilation and Referral for Aortic Surgery in Marfan Syndrome. Pediatr Cardiol. 2018 Oct;39(7):1453-1461. doi:10.1007/s00246-018-1916-6. Epub 2018 Jun 11. PubMed PMID: 29948025; PubMed Central PMCID: PMC6150800.K Khush K, Cherikh WS, Chambers DC, Goldfarb S, Hayes D Jr.,, Kucheryavaya AY, Levvey BJ, Meiser B, Rossano JW, Stehlik J; International Society for Heart and Lung Transplantation. The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Thirty-fifth Adult Heart Transplantation Report-2018; Focus Theme: Multiorgan Transplantation. J Heart Lung Transplant. 2018 Oct;37(10):1155-1168. doi: 10.1016/j.healun.2018.07.022. Epub 2018 Aug 10. PubMed PMID: 30293612.

Kenny D, Rhodes JF, Fleming GA, Kar S, Zahn EM, Vincent J, Shirali GS, Gorelick J, Fogel MA, Fahey JT, Kim DW, Babaliaros VC, Armstrong AK, Hijazi ZM. 3-Year Outcomes of the Edwards SAPIEN Transcatheter Heart Valve for Conduit Failure in the Pulmonary Position From the COMPASSION Multicenter Clinical Trial. JACC Cardiovasc Interv. 2018 Oct 8;11(19):1920-1929. doi: 10.1016/j.jcin.2018.06.001. PubMed PMID:30286853.

Lasso A, Nam HH, Dinh PV, Pinter C, Fillion-Robin JC, Pieper S, Jhaveri S, Vimort JB, Martin K, Asselin M, McGowan FX, Kikinis R, Fichtinger G, Jolley MA. Interaction with Volume-Rendered Three-Dimensional Echocardiographic Images in Virtual Reality. J Am Soc Echocardiogr. 2018 Oct;31(10):1158-1160. doi: 10.1016/j.echo.2018.06.011. Epub 2018 Aug 6. PubMed PMID: 30093145.

Liu MY, Zielonka B, Snarr BS, Zhang X, Gaynor JW, Rychik J. Longitudinal Assessment of Outcome From Prenatal Diagnosis Through Fontan Operation for Over 500 Fetuses With Single Ventricle-Type Congenital Heart Disease: The Philadelphia Fetus-to-Fontan Cohort Study. J Am Heart Assoc. 2018 Oct 2;7(19):e009145. doi:10.1161/JAHA.118.009145. PubMed PMID: 30371305.

Lynch JM, Ko T, Busch DR, Newland JJ, Winters ME, Mensah-Brown K, Boorady TW, Xiao R, Nicolson SC, Montenegro LM, Gaynor JW, Spray TL, Yodh AG, Naim MY, Licht DJ. Preoperative cerebral hemodynamics from birth to surgery in neonates with critical congenital heart disease. J Thorac Cardiovasc Surg. 2018 Oct;156(4):1657-1664. doi:10.1016/j.jtcvs.2018.04.098. Epub 2018 May 3. PubMed PMID: 29859676; PubMedCentral PMCID: PMC6166233.

Mah DY, Sleeper LA, Crosson JE, Czosek RJ, Love BA, McCrindle BW, Muiño-Mosquera L, Olson AK, Pilcher TA, Tierney ESS, Shah MJ, Wechsler SB, Young LT, Lacro RV. Frequency of Ventricular Arrhythmias and Other Rhythm Abnormalities in Children and Young Adults With the Marfan Syndrome. Am J Cardiol. 2018 Oct 15;122(8):1429-1436. doi: 10.1016/j.amjcard.2018.07.006. Epub 2018 Jul 17. PubMed PMID: 30115424.

Mercer-Rosa L, Fogel MA, Paridon SM, Rychik J, Yang W, Goldmuntz E. Revisiting the End Diastolic Forward Flow (Restrictive Physiology) in Tetralogy of Fallot: An Exercise, Echocardiographic, and Magnetic Resonance Study. JACC Cardiovasc Imaging. 2018 Oct;11(10):1547-1548. doi: 10.1016/j.jcmg.2018.01.008. Epub 2018 Mar 14. PubMed PMID: 29550323.

Rossano JW, Cherikh WS, Chambers DC, Goldfarb S, Hayes D Jr, Khush KK, Kucheryavaya AY, Toll AE, Levvey BJ, Meiser B, Stehlik J. The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Twenty-first pediatric heart transplantation report-2018; Focus theme: Multiorgan Transplantation. J Heart Lung Transplant. 2018 Oct;37(10):1184-1195. doi:10.1016/j.healun.2018.07.018. Epub 2018 Aug 8. PubMed PMID: 30293614.

Szwast A, Putt M, Gaynor JW, Licht DJ, Rychik J. Cerebrovascular response to maternal hyperoxygenation in fetuses with hypoplastic left heart syndrome depends on gestational age and baseline cerebrovascular resistance. Ultrasound Obstet Gynecol. 2018 Oct;52(4):473-478. doi: 10.1002/uog.18919. Epub 2018 Sep 3. PubMed PMID: 28976608.

Unolt M, Versacci P, Anaclerio S, Lambiase C, Calcagni G, Trezzi M, Carotti A, Crowley TB, Zackai EH, Goldmuntz E, Gaynor JW, Digilio MC, McDonald-McGinn DM, Marino B. Congenital heart diseases and cardiovascular abnormalities in 22q11.2 deletion syndrome: From well-established knowledge to new frontiers. Am J Med Genet A. 2018 Oct;176(10):2087-2098. doi: 10.1002/ajmg.a.38662. Epub 2018 Apr 16. Review. PubMed PMID: 29663641.